TY - JOUR
T1 - Hybrid trans-apical atrioventricular valve-in-valve implantation in Fontan circulation
AU - Butera, Gianfranco
AU - Lucchese, Gianluca
AU - Austin, Conal
AU - Frigiola, Alessandra
PY - 2020/4/1
Y1 - 2020/4/1
N2 - Trans-apical approach has been proved successful in failing surgical bio-prosthesis in both mitral and aortic position in adult patients. Recently, valve-in-valve treatments have been applied even in patients with complex congenital heart disease. Here, we report the case of a 32 years old lady with left atrial isomerism, complete AV septal defect, interrupted inferior vena cava with azygos continuation who underwent Kawashima procedure with atrial Fontan. Severe systemic atrioventricular valve regurgitation necessitated a 33 mm Perimount valve implantation and conversion to lateral tunnel Fontan. After only 4 years there was severe valve stenosis and the patient underwent successful trans-apical transcatheter implantation of a 29 mm Sapien valve.
AB - Trans-apical approach has been proved successful in failing surgical bio-prosthesis in both mitral and aortic position in adult patients. Recently, valve-in-valve treatments have been applied even in patients with complex congenital heart disease. Here, we report the case of a 32 years old lady with left atrial isomerism, complete AV septal defect, interrupted inferior vena cava with azygos continuation who underwent Kawashima procedure with atrial Fontan. Severe systemic atrioventricular valve regurgitation necessitated a 33 mm Perimount valve implantation and conversion to lateral tunnel Fontan. After only 4 years there was severe valve stenosis and the patient underwent successful trans-apical transcatheter implantation of a 29 mm Sapien valve.
KW - atrioventricular valve replacement
KW - Fontan circulation
KW - total cavopulmonary connection
KW - transcatheter valve-in-valve implantation
UR - http://www.scopus.com/inward/record.url?scp=85077872983&partnerID=8YFLogxK
U2 - 10.1002/ccd.28714
DO - 10.1002/ccd.28714
M3 - Article
C2 - 31912986
AN - SCOPUS:85077872983
SN - 1522-1946
VL - 95
SP - 950
EP - 953
JO - CATHETERIZATION AND CARDIOVASCULAR INTERVENTIONS
JF - CATHETERIZATION AND CARDIOVASCULAR INTERVENTIONS
IS - 5
ER -