Liver resection for the treatment of a congenital intrahepatic portosystemic venous shunt

TY - JOUR

T1 - Liver resection for the treatment of a congenital intrahepatic portosystemic venous shunt

AU - Papamichail, Michail

AU - Ali, Amir

AU - Quaglia, Alberto

AU - Karani, John

AU - Heaton, Nigel

PY - 2016/6

Y1 - 2016/6

N2 - Intrahepatic portosystemic shunts (IPSS) are rare congenital anomalies arising from disordered portal vein embryogenesis. It has been described in both children and adults and may be asymptomatic or be associated with a variety of neurophysiological and pulmonary complications. When recognized, early intervention to occlude the shunt will reverse the associated complications. Literature review reports of surgical and radiological occlusion of the shunt, but due to its rarity, a standard therapeutic protocol has not been established. A case of a 38-year-old woman with abdominal pain and low grade encephalopathy, diagnosed with an IPSS and treated by right hepatectomy was reported.

AB - Intrahepatic portosystemic shunts (IPSS) are rare congenital anomalies arising from disordered portal vein embryogenesis. It has been described in both children and adults and may be asymptomatic or be associated with a variety of neurophysiological and pulmonary complications. When recognized, early intervention to occlude the shunt will reverse the associated complications. Literature review reports of surgical and radiological occlusion of the shunt, but due to its rarity, a standard therapeutic protocol has not been established. A case of a 38-year-old woman with abdominal pain and low grade encephalopathy, diagnosed with an IPSS and treated by right hepatectomy was reported.

KW - intrahepatic portosystemic shunt

KW - liver resection

U2 - 10.1016/S1499-3872

DO - 10.1016/S1499-3872

M3 - Literature review

SN - 1499-3872

VL - 15

SP - 329

EP - 333

JO - Hepatobiliary & Pancreatic Diseases International

JF - Hepatobiliary & Pancreatic Diseases International

IS - 3

ER -